Giant Thoracic Ganglioneuroma with Mass Effect: A Case Report

ZEGMOUT Adil, CHARAF Hanane, BOUCAID Abdelhalim, AMCHICH Youness, SOUHI Hicham, OUAZZANI Hanane EL, RHORFI Ismail Abderrahmane, ABID Ahmed
2020 International Journal of Pediatric Research  
Thoracic ganglioneuromas are exceedingly rare. They arise from neural crest cells. These tumors are mostly asymptomatic, but massive tumors can present symptoms related to locoregional compression like dyspnea or scoliosis. We report a case of thoracic paravertebral giant ganglioneuroma in a 12-year-old child presenting as a large intrathoracic mass in the posterior mediastinum with intimate contact with the dorsal spine. That masse causes skeletal deformity and scoliosis. Scoliosis secondary
more » ... oliosis secondary to ganglioneuroma is rare and there is no report on its incidence. The diagnosis was made on a CT-guided tarnsparietal biopsy. Our intent is to highlighting the difficulties that may occur during the diagnosis of such patients, especially in view of the unusual clinical signs and the large size of the tumor. As well as the management of paravertebral ganglioneuroma associated with scoliosis, especially in the preoperative phase. CASE REpORT Check for updates and analysis of the case improved the knowledge of this tumor. Observation A 12-year-old child without a medical history significant, had been presented witha progressive shortness of breath without other respiratory or extra respiratory associated signs. The child had no loss of weight, and his appetite was good. The clinical examination objectified the presence of a scoliosis attitude and a condensation syndrome of the right hemithorax, there were no abnormalities on nervous system examination. A chest X -ray revealed a large round opacity occu-
doi:10.23937/2469-5769/1510061 fatcat:rtq5qwtaanfzngmu6x5b7ibv54