Pulmonary Intralobar sequestration Six cases of pulmonary intralobar sequestration observed between 1965 and 1979 are presented. Ages ranged form 6 months to 11 years. The duration of symptoms prior to diagnosis was from 11 months to 3 years. The clinical picture was polymorphous:3 cases were asymptomatic, 2 had respiratory signs and 1 had prolonged fever suggesting infection, Pulmonary signs were discrete and out of proportion with radiological findings. The latter showed consolidations in the

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... posterior basal segments of the left inferior lobe. In 5 cases there were mediastinal shifts toward the opposite side. In 3 patients airfluid levels were seen in the affected area. All cases were studied with bronchography and aortography which were diagnostic. Treatment consisted in left inferior lobectomy in all cases, with a favourable outcome. Pathology disclosed presence of non functional parenchima excluded form the normal respiratory tract. The anomalous vessels originated from thoracic (3) or abdominal aorta (3) and were single (3) or multiple (3) . Differencial diagnosis and clinical-radiological considerations are commented. The importance of aortography and surgical treatment is emphasized. La secuestracion pulmonar es una malformation congenita caracterizada por la presencia de tejido pulmonar no funcional, habitualmente sin comunicacion bronquial con el arbol respiratorio normal, que posee irrigation arterial sistemica a traves de uno o mas vasos anomalos, procedentes de la aorta toracica o abdominal o alguna de sus ram as. Existen dos tipos de secuestracion: Intralobar, en la cual el tejido pulmonar anomalo esta incluido dentro de la tabulation pulmonar normal y con retorno venoso predominantemente hacia las venas pulmonares inferiores. Extralobar,.cuando la malformation esta sepa-Dpto. Broncopulmonares. Hospital Paula Jaraquemada. Servicio de Anatomia Patologica. Hospital Paula Jaraquemada. Servicio de Cirugi'a infantil. Hospital Paula Jaraquernada. rada del tejido pulmonar normal, posee una envoltura pleural propia, se ubica en situation infra o supradiafragmatica, con retorno venoso habitualmente hacia el sistema azigos. La secuestracion pulmonar intralobar es aproximadamente seis veces mas frecuente que la extralobar, constituyendo ambas una enfermedad pulmonar poco frecuente, que se traduce en poco mas de 400 casos comunicados hasta 1978 en la literatura mundial(l). En nuestra bibliograffa pediatrica national hemos encontrado la description de 5 casos (2 intra y 3 extralobares). (2, 3) , Etiopatogenicamente, el origen de esta entidad no se encuentra definitivamente aclarado. Predomina la opinion acerca de su caracter congenito, relacionado con modificaciones del brote pulmonar en etapas precoces de la embriogenesis (4, 5, 6, 7), a traves de un proceso, por el cual un elemento vascular anormal ejerceria atraccion sobre una zona del pulmon en desarrollo, determinando como resultante esta malformacion. (Teori'a de Pryce). 431