Case Scenario: Metastatic Pediatric Paraganglioma Presenting during the Course of an Elective Surgery

Barak Cohen, Aviel Silbiger, Sorina Otremski, Idit Matot
2011 Anesthesiology  
P HEOCHROMOCYTOMA and paraganglioma are neuroendocrine tumors rarely diagnosed in pediatric patients. 1, 2 The incidence of malignant pheochromocytoma and paraganglioma in childhood is approximately 0.02 cases per million every year. 3, 4 Coincidental intraoperative diagnosis of pheochromocytoma involves very high mortality rates, reaching 50%. 5 We present a case of coincidental diagnosis of pediatric metastatic malignant paraganglioma during an elective surgical procedure. The evaluation and
more » ... anagement of pheochromocytoma and paraganglioma are discussed.
doi:10.1097/aln.0b013e318222ac2a pmid:21720240 fatcat:6cjghweehbgcrje3nxiuizrsum