Primary idiopathic intracranial hypertension (IIH), previously termed pseudotumor cerebri, is characterized by an elevated cerebrospinal fluid pressure of no identified cause. IIH is essentially a diagnosis of exclusion, suspected by clinical signs and supported by imaging findings with additional tests to rule out secondary causes of raised intracranial pressure. IIH occurs mainly in adults and may also be found in adolescents. Data on IIH in children remain sparse. The aim of this report was

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... o describe the clinical picture and outcome of 5 young children (age <1-4 years) who presented to our tertiary medical center with various complaints and were found on comprehensive evaluation to have IIH. We found that IIH in this age group poses a diagnostic challenge. It often has a different clinical picture from adult IIH, follows a more complicated course, and responds poorly to treatment with Acetazolamide. Larger prospective studies are needed.