Cystic Cervical Dysraphism: A Single Institution Experience and Outcome from a Case Series

MOHAMED GABR, M.D.; MOHAMED R. NAGY, M.D., AHMED A. ABDULLAH, M.D.
2022 The Medical journal of Cairo University  
Cystic cervical dysraphism is considered a rare entity. It has more frequent congenital anomalies than their lumbosacral variety. Most of these lesions are symptomatic in childhood period due to progressive tethering of spinal cord or nerve root. Material and Methods: This is a retrospective study of all cases underwent surgery for cystic cervical dysraphism from July 2016 to July 2021 at the Aburish Pediatric Hospital, Cairo University. All patients were neurologically and radiologically
more » ... ed. Neurological outcome was noted at the last follow-up. Results: Twelve children (7 females and 5 males) were operated upon. The mean age was 20.8±13.8 (range, 4-48) months. Meningocele was found in five patients (41.7%). Other five children (41.7%) had a thick stalk with lipomatous nodular swelling. One patient (8.3%) had myelocystocele. Another patient (8.3%) was suffering from myelomeningocele. Five cases were hydrocephalic; two of them underwent ventriculoperitoneal shunt insertion prior to surgery. Associated anomalies were present in nine children (75%). For the neurological outcome, we have noted no signs of neurological deterioration after surgery in all patients. Conclusions: Provided that there is no or minimal neurological deterioration at time of presentation, the outcome of surgery for cystic cervical dysraphism is excellent. The surgery helps in improving the cosmetic results, preventing the development of further neurological deterioration, and minimizing the infection. This is achieved mostly by efficient untethering.
doi:10.21608/mjcu.2022.234961 fatcat:byrlo4wbmbahblyh2pklc6raum