Behçet's disease is a relapsing vasculitis of unknown etiology, characterized by oral ulcers, genital ulcers, skin lesions, intraocular inflammation, and other organ involvement 1) . Central nervous system (CNS) involvement in Behçet's disease has a significant impact on patient prognosis and quality of life, and this condition is known as neuro-Behçet's syndrome. In most cases, neuro-Behçet's syndrome is characterized by aseptic meningitis, cerebellar signs, intracranial hypertension, and

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... idal alterations. Generally, CNS involvement is observed in about 3%-10% of patients with Behçet's disease; however, CNS involvement was found at autopsy in 34% of Japanese patients with the disease, so it is estimated that such involvement occurs more frequently than expected in these patients 2) . According This report was presented as a poster at the 64 th Annual Autumn Meeting of the Korean Pediatrics Society, 2014.