Nervous system involvement in Degos disease

Carmelo Amato, Raffaele Ferri, Maurizio Elia, Filomena Cosentino, Carmelo Schepis, Maddalena Siragusa, Massimo Moschini
<span title="">2005</span> <i title="American Society of Neuroradiology"> <a target="_blank" rel="noopener" href="" style="color: black;">American Journal of Neuroradiology</a> </i> &nbsp;
Degos disease, or malignant atrophic papulosis, is a rare obstructive vasculopathy of unknown origin, characterized by distinctive skin lesions, visceral involvement, and an unfavorable outcome. The gastrointestinal tract and the central nervous system are most frequently affected, but cases limited to benign skin lesions have also been described. Neuroradiologic reports of this condition are exceptionally rare. We report the case of a 29-year-old woman with central and peripheral nervous
more &raquo; ... involvement who presented with progressive clinical deterioration and a meningovascular pattern at cerebral MR imaging; other organs were spared in this patient.
<span class="external-identifiers"> <a target="_blank" rel="external noopener" href="">pmid:15760880</a> <a target="_blank" rel="external noopener" href="">pmcid:PMC7976473</a> <a target="_blank" rel="external noopener" href="">fatcat:2dck2o5pcbdffpk7qz4q45opqy</a> </span>
<a target="_blank" rel="noopener" href="" title="fulltext PDF download" data-goatcounter-click="serp-fulltext" data-goatcounter-title="serp-fulltext"> <button class="ui simple right pointing dropdown compact black labeled icon button serp-button"> <i class="icon ia-icon"></i> Web Archive [PDF] <div class="menu fulltext-thumbnail"> <img src="" alt="fulltext thumbnail" loading="lazy"> </div> </button> </a> <a target="_blank" rel="external noopener" href="" title="pubmed link"> <button class="ui compact blue labeled icon button serp-button"> <i class="file alternate outline icon"></i> </button> </a>