Intraosseous Neurofibroma and Concurrent Involvement of the Mandible, Maxilla and Orbit: Report of a Case

Zahra Dalili, Gholamhossein Adham
2012 Iranian Journal of Radiology  
Neurofibroma is an autosomal dominant disorder which has major criteria such as hyperpigmentation (cafe-au lait spots), cutaneous and subcutaneous tumors and bone deformities. In this report, a case of multifocal intraosseous neurofibroma in a 16-year-old male with right facial asymmetry, multiple unerupted maxillary posterior teeth and a previous history of infratemporal and orbital neurofibroma is presented. The majority of reported cases occurred in the posterior portion of the mandible and
more » ... limited number in the maxilla. Cone beam CT (CBCT) was performed for better evaluation of the extension and form of the maxillary and mandibular lesions. This report presents a rare situation of simultaneous peripheral neurofibromatosis (NF) and multifocal intraosseous NF in the mandible, maxilla and orbits and also focuses on advanced imaging findings of bony and soft tissue neurofibroma.
doi:10.5812/iranjradiol.6684 pmid:23329961 pmcid:PMC3522340 fatcat:lwlc77z6j5hanjrmflfnnshkwe