Respiratory support in the absence of abdominal muscles: a case study of ventilatory management in prune belly syndrome

Heleen JCL Apostel, Els LIM Duval, Jozef J De Dooy, Philippe G Jorens, Tom Schepens
2020 Paediatric Respiratory Reviews  
Prune belly syndrome (PBS) results in a total lack of abdominal musculature. Abdominal muscles have an important function during inspiration and expiration. This puts the patient at risk for respiratory complications since they have a very limited ability to cough up secretions. Patients in an intensive care unit (ICU) with PBS who receive mechanical ventilation are at even greater risk for respiratory complications. We review the function of the abdominal muscles in breathing and delineate why
more » ... g and delineate why they are important in the ICU. We include an illustrative case of a long-term ventilated patient with PBS and offer respiratory management options.
doi:10.1016/j.prrv.2020.07.002 pmid:33349558 fatcat:knsm4ovdjbgv5bdxolktracwsm