Lung transplantation as a viable option of treatment for pulmonary veno-occlusive disease

Marek Ochman, Maciej Urlik, Zofia Tatoj, Marta Wajda-Pokrontka, Fryderyk Zawadzki, Magdalena Latos, Marian Zembala
2018 Advances in Respiratory Medicine  
Pulmonary veno-occlusive disease (PVOD) is a rare form of pulmonary hypertension caused by alteration of pulmonary veins. Many clinical and hemodynamic similarities to idiopathic pulmonary arterial hypertension (IPAH) may cause diagnostic and therapeutic difficulties. This case report is about a patient with PVOD, whose first symptoms of the disease occurred after infectious mononucleosis. The patient was administered prostacycline (PGI2) mimetic (Treprostinil), which made qualification process
more » ... and lung transplantation possible. Despite more and more knowledge about the causes, ethiopathogenesis and changes in pulmonary veins on molecular level, lung transplantation is the only successful therapeutic option for patients suffering from PVOD.
doi:10.5603/arm.2018.0040 fatcat:d7po62xptzbfjkyb7ojuqf56ta