Alstrom syndrome: A case report

Fatma Koray, Can Dorter, Yasemin Benderli, Ílhan Satman, Temel Yilmaz, Nevin Dinccag, Kubilay Karsidag
2001 Journal of Oral Science  
Alstrom syndrome is a rare disorder characterized by early obesity, loss of central vision, diabetes mellitus, hearing loss and short stature. Previous studies, have reported no information regarding oral findings. This article describes oral findings in two cases of Alstrom syndrome. In both cases, gingivitis was present and also light yellowbrown discolored enamel bands were observed on the anterior teeth. This staining may have resulted from discoloration of the preexisting slight band-like
more » ... namel hypoplasia. The gingiva was examined histologically by light and transmission electron microscopy. Irregular thickness of the basal lamina and delamination of the myelin sheath were detected by transmission electron microscopy. There is no information about pathological odontogenesis in Alstrom syndrome in previous reports. Oral present findings may contribute further information about the clinical manifestations of Alstrom syndrome. (J. Oral Sci. 43, 221-224, 2001)
doi:10.2334/josnusd.43.221 fatcat:6elqjnmgtjat5mkdg3wnneathm