Mesenteric Vein Thrombosis Due to Protein S Deficiency in a Girl

YAMAN Aytaç; KULOĞLU
2014 Ankara Üniversitesi Tıp Fakültesi Mecmuası  
Mesenteric venous thrombosis (MVT) is a very rare condition in children, and may cause bowel infarction and gangrene. It may be caused by congenital or acquired factors, including protein S deficiency; a very rare genetic disorder. Here we report a case of MVT in a girl with protein S deficiency. The patient developed splenic necrosis and massive small bowel infarction sparing the colon. Contrast enhanced computed tomography led to prompt diagnosis of small bowel and splenic necrosis. The
more » ... necrosis. The patient was treated successfully by resection of the necrotic bowel and anticoagulant therapy.
doi:10.1501/tipfak_0000000861 fatcat:prprkviiwfd5tbfmmw7lmivymi