Pleuropulmonary Blastoma in Pediatric Age Group: A Very Rare Case Report and Review of Literature

Kalpesh Onkar Patil
2020 Open Journal of Pediatrics  
Pleuropulmonary blastoma (PPB) is a very rare and very aggressive malignant tumor that affects children and adults. Though its presentation in children has been reported in literature, incidence is very low as compared to adults. This neoplasm is characterized on histology by primitive blastema and a malignant mesenchymal stroma that often demonstrates multidirectional differentiation. Even though availability of multimodal therapy, the prognosis of patients with PPB remains poor.
doi:10.4236/ojped.2020.101009 fatcat:ilt25wt4avgxhdpsosbzc3nrwe