Tumor hepático con vías biliares normales en un paciente con síndrome de Alagille: a propósito de un caso

2015 Archivos Argentinos de Pediatria  
This manuscript reports a case of a patient with Alagille syndrome who developed a rapidly growing lesion in the caudate segment of his cirrhotic liver. This mass was closely monitored but did not seem malignant from a radiological point of view. An MRI showed no criteria in favour of a hepatocarcinoma, however, the rapid growth lead to a biopsy of both the lesion and the cirrhotic liver. The pathology results indicated normal development of the bile ducts in the mass and paucity of the biliary
more » ... city of the biliary ducts in the second liver specimen. We will describe this case and propose an interpretation of these findings.
doi:10.5546/aap.2015.e223 pmid:26172023 fatcat:5t5b5awbfneobdnp5dzcuiujrm