A Case of Antiphospholipid Antibody Syndrome Accompanied by Valvular Heart Disease and Moya Moya Syndrome

Sung Ho Choi, Bo Young Joung, Dongsoo Kim, Jae Phil Choi, Min Ho Cho, Sung Ju Lee, Sang Hak Lee, Byung Eun Park, Bum Kee Hong, Hyuck Moon Kwon, Chanil Park, Tae Sub Chung (+1 others)
2003 Korean Circulation Journal  
A case of antiphospholipid antibody syndrome, accompanied by valvular heart disease and Moya moya syndrome, has never been reported. Here, we report on a case that had mitral regurgitation and Moya moya syndrome, associated with antiphospholipid antibody syndrome secondary to systemic lupus erythematosus. This patient underwent a mitral valve replacement for mitral valve regurgitation. The postoperative course was uneventful, and the pathological findings of the mitral valve showed a
more » ... showed a degenerative change, due to chronic inflammation, a proliferative fibrous change and calcification, but without thrombus formation. However, the patient returned to the hospital with a cerebral hemorrhage, which was caused by Moya moya syndrome. Surgical drainage was performed, and the patient was discharged without any complications. The patient is on anticoagulation and immunosuppression drugs, with no problems to date. (Korean Circulation J 2003 ; 33 (7) : 620-624) KEY WORDS:Antiphospholipid syndrome;Lupus erythematosus, systemic;Heart valve disease;Moyamoya disease.
doi:10.4070/kcj.2003.33.7.620 fatcat:pnhr7eo4gregvo4cnsc3jekiai