Case Report of Prosthetic Treatment of a Young Patient Suffering Papilon-Lefever Syndrome

Masoumeh Rostamzadeh, Ghasem Omati Shabestari, Mohammad Rastegar Khosravi
2017 International journal of clinical medicine  
Papillon-Lefevre syndrome (PLS) is a rare recessive autosomal disease which occurs with palms and soles hyperkeratosis as well as primary and permanent teeth periodontal loss. Recently, it has been proved that a mutation at Cathepsin gene C is the genetic cause of PLS. All primary and permanent teeth of the patients are lost at ages 2 or 3 because of serious alveolar bone destruction. This paper presents a complete case of prosthetic treatment of an 8-year old girl with PLS.
doi:10.4236/ijcm.2017.86040 fatcat:mgexb2yh3bfmtigc66gxnmnfqq