Double outlet right ventricle with absent infundibular septum and common ventriculo-arterial valve

Paolo Ciliberti, Aurelio Secinaro, Gabriele Rinelli, Alessia Del Pasqua, Adriano Carotti
2017 Cardiology Journal  
A 1-year-old male was referred to our unit because of double outlet right ventricle ( Fig. 1A) with d-transposition of the great arteries and restrictive ventricular septal defect (VSD), located in subpulmonary position, but effectively committed to both pulmonary and aortic outflows because of absent infundibular septum (see Fig. 1, arrow) . A first stage palliation had already been performed by atrial septectomy and pulmonary arterial banding. Preoperative cardiac magnetic resonance imaging
more » ... owed complete absence of the infundibular septum (Fig. 1A , red asterisk) and fibrous continuity between the pulmonary and aortic valves (Fig. 1B) . The tricuspid aortic valve was anterior to the right of the bicuspid pulmonary valve (Fig. 1C) . The echocardiogram (Fig. 1D ) also suspected partial Figure 1. Cardiac magnetic resonance imaging (A, B, C) and echocardiographic (D) anatomical findings; AO -aorta; LV -left ventricle; RV -right ventricle; PA -pulmonary artery. A C B D
doi:10.5603/cj.2017.0042 pmid:28421590 fatcat:4n2zrzserrgzth2n7qvosdpfuu