Ectopia Cordis: A Rare Congenital Heart Disease

Naharuma Aive Hyder Chowdhury, Mohammad Sharifuzzaman, Mohammad Abul Kalam Azad, Tuhin Haque, Jesmin Hossain
2019 Cardiovascular Journal  
Three days old female presented with beating heart outside the thoracic cavity. This is a rare congenital abnormality associated multiple abnormalities. Patient came with features of infection. To diagnose routine blood investigation along with echocardiography and CT angiogram of heart,great vessel and abdomen were done. She was diagnosed as functionally single ventricle with hypoplastic branch pulmonary artery with malposed great artery with anomalous pulmonary venous drainage. Thisis lethal
more » ... age. Thisis lethal variety of ectopic cordis. Our patient had no adequate space in mediastinum to replace heart and she was in septicemia, so managed medically. Patient expired at her 6thday due to sepsis and intracardiac complex congenital heart disease. Cardiovasc. j. 2019; 11(2): 183-186
doi:10.3329/cardio.v11i2.40419 fatcat:anxuf3p5dzc7vm4dsid24vdpia