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Morquio syndrome (MS) or mucopolysaccharidosis (MPS) type IVA is a progressive lysosomal storage disorder with autosomal recessive inheritance. Deficiency of enzymes N-acetyl-galactosamine-6-sulphatase and beta-galactosidase which compromises the catabolism of the glycosaminoglycans (GAGs) leads to excessive accumulation of GAGs in soft tissue, cartilage and bone causing severe skeletal dysplasia and difficult airway. Other systems commonly involved systems are cardiovascular, respiratory,doi:10.18203/2320-6012.ijrms20210898 fatcat:ehgbgpf4jvgdjlklwf66tb75s4