A case of perivascular epithelioid cell tumor of the palatine mucosa

Noriko KOMATSU, Takahiro ABE, Rena SHIRAI, Asako TANIGUCHI, Masanobu ABE, Kazuto HOSHI
2020 Japanese Journal of Oral & Maxillofacial Surgery  
Perivascular epithelioid cell tumor: PEComa is a group of tumors defined in the WHO classification of bone and soft tissue tumors as "mesenchymal tumors consisting of cells that are associated with blood vessel walls and express markers of melanocytes and smooth muscle" . We report a case of soft palate PEComa. The patient was a 17-year-old boy. The diagnosis of hemangiomatous fibrotic histiocytoma, which is considered to be a benign malignant intermediate tumor, was obtained at a previous
more » ... at a previous doctor, and the patient was referred to our department because of the need for multidisciplinary treatment. A mass lesion with an ulcer was found in the midline of the soft palate. Contrast-enhanced MRI showed the findings of the separated nodule image in the soft palate. Preoperative evaluation of the previous specimen confirmed the diagnosis of PEComa. Since this case was a benign tumor with a relatively good prognosis, we performed resection with consideration for functional preservation. Although one year has passed since surgery, the patient has progressed well without recurrence. PEComa is extremely rare in the oral cavity. This is considered a valuable case for accumulating information in the future. : PEComa (血管周囲類上皮細胞腫瘍) 1) 東京大学医学部附属病院口腔顎顔面外科・矯正歯科 (主任:星 和人教授) 2) 国際医療福祉大学三田病院歯科口腔外科 (主任:矢郷 香部長) 1)
doi:10.5794/jjoms.66.371 fatcat:m3h4qamfc5gcxntes3ximsy64i