Polysplenia Syndrome with Various Visceral Anomalies in an Adult: Embryological and Clinical Considerations

Shinjiro MUNETA, Shuji SAKAI, Hiroshi FUKUDA, Yoichi IMAMURA, Isao MATSUMOTO
1992 Internal medicine (Tokyo. 1992)  
A 26-year-old female with polysplenia syndrome is reported. She had numerous visceral anomalies including polysplenia, a short pancreas, a preduodenal portal vein, malrotation of the bowel, azygos continuation of the inferior vena cava, bilateral hyparterial bronchi and symmetrical liver lobation. Embryological and clinical considerations of polysplenia syndrome are described. (Internal Medicine 31: 1026-1031 Key words: short pancreas, preduodenal portal vein, azygos continuation of the
more » ... vena cava, bilateral hyparterial bronchi, malrotation of the bowel From
doi:10.2169/internalmedicine.31.1026 fatcat:xms2imxmhjh73oags6j2ea6k4i