Congenital diaphragmatic hernia (CDH) is sometimes seen in siblings but is rarely seen in twins, and five survived cases of CDH in monozygotic or dizygotic twins have been reported in the English literature. Here we report a sixth survived case of CDH in dizygotic twins which was prenatally diagnosed as a very severe type and was successfully treated by our intensive care team composed of obstetricians, neonatologists, surgeons and anesthesiologists.