Pulmonary valve stenosis (PS) is the 3rd most common form of adult congenital heart disease. The patient was a 56-year-old woman, with known congenital heart disease but who was not receiving any treatment as she was not functionally limited. A two-dimensional echocardiogram showed severe right ventricular hypertrophy, pulmonary valve thickening and systolic doming. A color Doppler revealed a retrograde flow from the aorta to the left pulmonary artery. She had severe heart failure on the right

more »

... and side from a PS but did not display any symptoms. We hypothesized that she had a retrograde flow to the pulmonary circulation through a patent ductus arteriosus (PDA), through which oxygenated blood could be supplied to the systemic circulation and, hence, no hypoxia. We attempted a balloon valvuloplasty for the PS followed by a device closure for the PDA. Here we report on this adult female with severe PS but lacking any symptoms, due to the presence of a PDA. ( Korean J Med 2013;85:406-410) Keywords: Pulmonary valve Stenosis; Patent foramen ovale; Patent ductus arteriosus 서 론 폐동맥판협착은 소아 선천성 심질환의 10%를 차지하며[1] 대부분은 단독으로 나타나지만 팔로4징, 폐동맥협착증, 총동 맥간증 등이 복합된 중증 선천성 심질환 형태로 나타나기도 한다. 질병은 양성 경과를 보이며 대부분은 성인까지 생존하 지만 정기적인 검진이 필요하며 중증의 폐동맥판협착은 우 심실부전에 의한 증상을 동반하게 되고 중재적 시술이나 수 술적 치료를 필요로 한다. 폐동맥협착증과 난원공개존증이 동반된 증례에서 중재적 시술을 통해 성인기까지 생존한 경 우는 있으나 동맥관개존증이 동반되어 성인까지 무증상으로 중재적 시술이나 수술적 치료 없이 생존한 경우는 아직 보