Polysplenia syndrome is anomaly associated with multiple spleens and anomalies of chest and abdominal organs. We present a case of polysplenia syndrome found in a 27-year-old man. Only those with mild anatomical abnormalities reach adulthood without a diagnosis. Radiological examinations are helpful to the diagnosis by showing the location and aspect of spleen, location of other organs in the abdomen, and identification of other associated anomalies. In this article, we illustrate anomalies of polysplenia syndrome and focus on abdominal organs.