Management of respiratory complications and rehabilitation in individuals with muscular dystrophies: 1st Consensus Conference report from UILDM - Italian Muscular Dystrophy Association (Milan, January 25-26, 2019)

Fabrizio Rao, Giancarlo Garuti, Michele Vitacca, Paolo Banfi, Fabrizio Racca, Renato Cutrera, Martino Pavone, Marina Pedemonte, Matteo Schisano, Stefania Pedroni, Jacopo Casiraghi, Andrea Vianello (+1 others)
2021 Acta myologica  
Respiratory complications are common in the patient with muscular dystrophy. The periodic clinical and instrumental respiratory evaluation is extremely important. Despite the presence in the literature of updated guidelines, patient associations often report lack of knowledge of these pathologies, particularly in peripheral hospitals. The purpose of this work, inspired by the Italian Muscular Dystrophy Association (UILDM) is to improve management of respiratory problems necessary for the
more » ... ent of these patients complex. To this end, the main items that the specialist can meet in the follow-up of these pathologies have been analyzed and discussed, among which the respiratory basal evaluation, the criteria of adaptation to non-invasive ventilation, management of bronchial secretions, situations of respiratory emergency, indications for tracheostomy and the subject of advance directives of treatment (DAT).
doi:10.36185/2532-1900-045 pmid:33870094 pmcid:PMC8033426 fatcat:jxh6u2cuireshoterqdlbheb2e